Electroencephalogram and clinical manifestations of Rett syndrome in children
| Main Authors: | Herini, E S, Mangunatmadja, I, S, Purboyo, Pusponegoro, Hardiono D, Sunartini, Sunartini |
|---|---|
| Format: | Article info application/pdf eArticle |
| Bahasa: | eng |
| Terbitan: |
Indonesian Pediatric Society
, 2016
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| Online Access: |
https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674 https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674/530 |
| ctrlnum |
article-674 |
|---|---|
| fullrecord |
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<dc schemaLocation="http://www.openarchives.org/OAI/2.0/oai_dc/ http://www.openarchives.org/OAI/2.0/oai_dc.xsd"><title lang="en-US">Electroencephalogram and clinical manifestations of Rett syndrome in children</title><creator>Herini, E S</creator><creator>Mangunatmadja, I</creator><creator>S, Purboyo</creator><creator>Pusponegoro, Hardiono D</creator><creator>Sunartini, Sunartini</creator><description lang="en-US">Background Rett Syndrome (RS) is a severe neurodevelopmentaldisorder. Epileptic seizures occur in 80-90%; grandmal, psychomo-tor (complex partial), and focal motor seizures have been reported.The electroencephalogram(EEG) is almost always abnormal.Objective This study aimed to investigate the EEG and clinicalmanifestations of children with RSResults We investigated EEG on 5 patients with RS aged 30–66month. One patient was in clinical stage II and 4 patients in clini-cal stage III. Four patients had history of seizures, however onlytwo patients suffered from epilepsy. The EEG demonstrated slow-ing background activity in occipital region in two patients. In addi-tion, epileptic form activities were observed in 4 of 5 patients.Conclusion We concluded that epileptic spike discharge with orwithout clinical seizures were found in almost all of our RS pa-tients. These paroxysmal discharges suggested the process andthe sequences of cortical involvement. Compelling clinical, neuro-physiological evidences were very important to decide the stageof Rett disorder</description><publisher lang="en-US">Indonesian Pediatric Society</publisher><date>2016-09-24</date><type>Journal:Article</type><type>Other:info:eu-repo/semantics/publishedVersion</type><type>File:application/pdf</type><identifier>https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674</identifier><identifier>10.14238/pi43.4.2003.121-5</identifier><source lang="en-US">Paediatrica Indonesiana; Vol 43 No 4 (2003): July 2003; 121-5</source><source>2338-476X</source><source>0030-9311</source><source>10.14238/pi43.4.2003</source><language>eng</language><relation>https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674/530</relation><recordID>article-674</recordID></dc>
|
| language |
eng |
| format |
Journal:Article Journal Other:info:eu-repo/semantics/publishedVersion Other File:application/pdf File Journal:eArticle |
| author |
Herini, E S Mangunatmadja, I S, Purboyo Pusponegoro, Hardiono D Sunartini, Sunartini |
| title |
Electroencephalogram and clinical manifestations of Rett syndrome in children |
| publisher |
Indonesian Pediatric Society |
| publishDate |
2016 |
| url |
https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674 https://paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/674/530 |
| contents |
Background Rett Syndrome (RS) is a severe neurodevelopmentaldisorder. Epileptic seizures occur in 80-90%; grandmal, psychomo-tor (complex partial), and focal motor seizures have been reported.The electroencephalogram(EEG) is almost always abnormal.Objective This study aimed to investigate the EEG and clinicalmanifestations of children with RSResults We investigated EEG on 5 patients with RS aged 30–66month. One patient was in clinical stage II and 4 patients in clini-cal stage III. Four patients had history of seizures, however onlytwo patients suffered from epilepsy. The EEG demonstrated slow-ing background activity in occipital region in two patients. In addi-tion, epileptic form activities were observed in 4 of 5 patients.Conclusion We concluded that epileptic spike discharge with orwithout clinical seizures were found in almost all of our RS pa-tients. These paroxysmal discharges suggested the process andthe sequences of cortical involvement. Compelling clinical, neuro-physiological evidences were very important to decide the stageof Rett disorder |
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IOS4351.article-674 |
| institution |
Ikatan Dokter Anak Indonesia (IDAI) |
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1183 |
| institution_type |
library:special library |
| library |
Badan Penerbit IDAI |
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1030 |
| collection |
Paediatrica Indonesiana |
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4351 |
| subject_area |
Pediatric/Pediatrik Newborn Infant, Neonates/Perawatan Bayi Baru Lahir, Neonatal |
| city |
JAKARTA PUSAT |
| province |
DKI JAKARTA |
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IOS4351 |
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2017-07-11T01:01:39Z |
| last_indexed |
2019-05-07T07:58:32Z |
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dc |
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1686120190542086144 |
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17.203505 |